Normal sex organ development and functioning is mainly dependent on the programming of the genes and on an adequate endocrine system in a healthy body. Sometimes nature (and man) errs so that sex organs are incomplete or aspects of both the male and female bodies are present. These resulting intersexes are usually problems to be dealt with by physicians but interesting questions arise that have a bearing on the study of sexual anomalies. For example, if a genetic woman is raised as a male, what is her object choice and/or gender identity? Will sexually anomalous behavior be present? This chapter examines these questions but for more complete medical information other sources should be consulted2529334749.
Physical sexual abnormalities stem from two main sources: from unusual hereditary in the genes and from an unusual endocrine system which produces sex hormones. The two are not independent. Usually anatomical sex is programmed in the X and Y chromosomes of the genes. These so called sex chromosomes are usually paired as XX or XY, one chromosome coming from each parent. an XX combination usually produces a normal female and the XY a normal male. One of at least 3 mistakes can occur: to many X's, too many Y's or only 1 X and no second X or Y chromosome. The major resulting genetic abnormalities are presented in Table 14.1.
In the case of the Triple X syndrome, no abnormalities of the external genitalia are necessarily evident but the female may be mentally retarded, have infantile genitalia, and she carries an unusual heredity. Similarly in the XYY syndrome, a physically normal and perhaps tall male results but he